Inozyme reports promising data on rare disease treatments

Published 01/10/2025, 09:18 PM
INZY
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BOSTON - Inozyme Pharma Inc. (NASDAQ:INZY), a clinical-stage biotech company with a current market capitalization of $180 million and strong liquidity position according to InvestingPro data, has announced positive interim results from its ENERGY 1 trial and Expanded Access Program (EAP), evaluating the investigational drug INZ-701 in infants and young children with ENPP1 Deficiency. The data revealed improvements in survival rates, heart function, and reductions in arterial calcifications and hypophosphatemia, with no serious treatment-related adverse events reported.

The ENERGY 1 trial and EAP assessed the efficacy of INZ-701 in patients with generalized arterial calcification of infancy (GACI), a severe form of ENPP1 Deficiency. While the company maintains a healthy current ratio of 7.68 and holds more cash than debt, InvestingPro analysis indicates rapid cash burn remains a key consideration for investors. The treatment led to an 80% survival rate beyond the first year for infants involved in the study, a significant increase compared to the historical 50% survival rate. Additionally, all surviving patients showed substantial reductions or stabilization in arterial calcifications, and improvements in left ventricular ejection fraction.

Inozyme has also completed enrollment for its ENERGY 3 pivotal trial in pediatric patients with ENPP1 Deficiency, with topline data expected in early 2026. The trial aims to support the use of INZ-701 in addressing rickets, a key clinical endpoint.

Moreover, the company has received regulatory guidance from both the FDA and EMA for its planned ASPIRE pivotal trial, which will focus on severe complications of ABCC6 Deficiency in children. The trial design received preliminary support from regulators, and Inozyme is refining the study protocol with plans to initiate the trial in early 2026.

ENPP1 Deficiency and ABCC6 Deficiency are rare genetic disorders that lead to serious health complications, including arterial calcifications, rickets, and cardiovascular issues. There are currently no approved therapies for these conditions.

The announcement is based on a press release statement from Inozyme Pharma Inc. and reflects the company's ongoing efforts to address unmet medical needs in the field of rare diseases affecting bone health and blood vessel function. With three analysts recently revising earnings estimates upward and the stock trading below InvestingPro's Fair Value estimate, investors seeking detailed analysis can access over 10 additional ProTips and comprehensive financial metrics through InvestingPro's platform.

In other recent news, Inozyme Pharma has been the subject of several analyst upgrades and has revealed promising interim data from its ongoing clinical trials. Jefferies initiated a Buy rating on Inozyme Pharma, highlighting the potential of its lead drug candidate, INZ-701. Piper Sandler also increased its target for Inozyme Pharma to $43, maintaining an Overweight rating on the company's shares. H.C. Wainwright reiterated a Buy rating and a $14.00 price target for Inozyme Pharma's shares.

Inozyme Pharma's lead drug candidate, INZ-701, is currently undergoing clinical trials. The Phase 2 studies have shown promising results, including the rapid normalization of pyrophosphate (PPi) levels in adults deficient in ENPP1 and ABCC6 enzymes. The company also plans to initiate a registrational trial for INZ-701 in calciphylaxis patients in 2025, pending regulatory approval and funding.

Recent developments include the appointment of Erik Harris to its Board of Directors and the announcement of approximately $23.8 million remaining in its at-the-market equity offering program, facilitated by Jefferies LLC. Furthermore, the company's third-quarter update revealed plans to release interim data from the ENERGY Phase 1b trial in the fourth quarter of 2024, with top-line results from the ENERGY 3 trial expected in early 2026.

These developments reflect the ongoing efforts of Inozyme Pharma in the biopharmaceutical sector. It's important to note that these updates are based on factual information and do not include personal opinions or predictions about the company's future performance.

This article was generated with the support of AI and reviewed by an editor. For more information see our T&C.

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